The chest series are characterised by an abnormal curving vascular structure that appears to get large as it approaches the diaphragm. In addition the volume of the right lung is smaller and there is anodd shape to the right hilum. The findings are consistent with a diagnosis of congenital hypoplasia of the right lung associated wth partial anomalous venous return to the IVC below the diaphragm. (aka congenital pulmonary venolobar syndrome) The curved anomalous vein is known as the scimitar sign since it has the shape of a scimitar.01714c03 Courtesy Ashley Davidoff MD |